CaafimaadkaCudurrada iyo Xaaladaha

Balanqaadyo Eastern - a ... curyaanimo Congenital. Valvular Cudurada Wadnaha

Congenital - waxa uu yahay waxan? Jawaabta su'aashan, waxaad ka articles soo bandhigay baran doonaan. Intaa waxaa dheer, waxaan kuu sheegi doonaa waxa noocyada cilladaha ka jira, sababta ay u horumariyaan, iyo wixii la mid ah.

macluumaad guud oo ku saabsan cilladaha lagu dhasho

Ku xigeenka - waa horumar aan caadi ahayn, sidoo kale ururinta wixii khaldama ka caadiga ah (standard) ee qaab-dhismeedka jidhka bini'aadamka ka dhaca inta lagu guda jiro horumarinta uurjiifka (dhalmada ka yar).

Sida caadiga ah, ka bedelida sida loo sameeyay sarkhaansan yihiin arrimo kala duwan dibadda iyo gudaha (tus, xanuunada hormoon, hiddo, unugyada jeermiga inferiority, caabuq fayras, ionizing shucaaca, ogsijiin la'aanta iyo wixii la mid ah.). Tan iyo markii qeybtii labaad ee qarnigii labaatanaad, khubaro bilaabeen inay aragto xawaaraha weyn oo ka mid ah isbedel bahal ah. cilladaha lagu dhasho badankood waxay ka dhacaan dadka ku nool dalalka horumaray.

sababo badan tahay

ma In 40-60% dadka ogaado sababaha leexashooyinkaasi of data. dheer bukaanka noocan oo kale ah waxay khusaysaa, taas oo u muuqataa sidii "cillado lagu dhasho goosgoos ah." hadal Tani waxa ay tilmaamaysaa dhacdo ee sababa shil dhacay ama aan la aqoon, iyo sidoo kale khatarta hoos u dib-u-dhacdo ka mid ah jiilka mustaqbalka.

Waayo, 20-25% ka mid ah kuwa cilladaha lagu dhasho loo sameeyay ka "multi-factor" keentaa, in uu yahay is dhexgalka adag cilladaha hiddo (badanaa yar) ama sababaha halista ah ee deegaanka. 10-13% ka mid ah cillado la xidhiidha oo kaliya in ay gaadhista deegaanka. Oo% ka mid ah cilladaha kaliya 12-25 yihiin oo keliya horumarinta hidaha ee Jidka.

Sidaas darteed, waxaanu ka fiirsan in faahfaahin dheeraad ah sababta ay dadku u gaar ah waa curyaanimo lagu dhasho.

teratogen

tallaabada arrimahaasi waxay ku xiran tahay qiyaasta. Khilaaf saamaynta teratogenic ee noocyada kala duwan la xiriirta in awoodda muuqaalada nuugid dheefshiidka walax si ay u dhexgalaan mandheerta iyo faafin jirka oo dhan.

Sababaha teratogenic ugu caansan oo bartay

Khalad waxaa inta badan lagu arko kuwa ku xiran yihiin in ay saamayn soo socda:

  • cudurrada faafa ee la soo maray hooyada in ilmaha caloosha ku. kala duwan oo ka mid ah cudurada viral sida wareejiyo inta lagu guda jiro iyo wallacaaga sida mumps, rubella ama inklyuzionnaya cytomegaly, iyo sidoo kale gacan ka laga yaabaa in iin horumarinta.
  • Khamriga. Muhiimad gaar ah waa Khamriga waalidka, ama halkii, hooyadiis. Cabitaanka khamriga inta ay uurka leedahay si fudud u keeni kartaa in uurjiifka khamriga syndrome.
  • Ionizing shucaaca. Gaadhista isotopes shucaaca, iyo sidoo kale X-rays saamayn taban ku leh qalab hidaha laga yaabaa in. Sidoo kale waa in la ogaadaa in shucaaca (ionizing) iyo leedahay saamayn sun. Taasi dhab ahaantii tani waa sababta ugu cillado lagu dhasho.
  • Daawooyinka. Si aad u taariikhda, ma jiraan wax daawo ah oo kale in la aqoonsan doono gebi ahaanba ammaan ah oo ilmaha caloosha ku, gaar ahaan inta lagu jiro labada trimester ugu horeeya uurka.
  • Nicotine. Qiiqa hooyooyinka mustaqbalka (xilliga uurka) si sahal ah waxay keeni kartaa in ay xaqiiqada ah in ilmaha ku dhici doonaan ka dambeeya in horumarka jireed.
  • yarida Nutrientnye. la'aanta ah ee tiro ka mid ah nafaqooyinka (tus, iodine, myo-inositol, folate iyo wixii la mid ah.) Ma arrin la xaqiijiyey khatarta cudurka wadnaha ee lagu dhasho iyo cilladaha tube neural.

Tixgeli logu talagalay this caadiga ah waa waalka iin qalbi si faahfaahsan weyn.

cilladaha wadnaha

cudurka wadnaha waa waalka ah pathologic isbedel, ma weelashii thoracic waaweyn, derbiyada wadnaha, taasoo keentay in dhiig carqaladeeyey dhaqdhaqaaqa caadiga ah. Waxaa la xusay in leexashooyinkaasi sida la mid heleen karaa ama lagu dhasho.

Inta badan, ka mada ka mid ah khaanadaha wadnaha dhacaan sabab u ah ciidamada xad dhaafka ah ee dagaalka difaaca ee jidhka bini'aadamka la dhex galay waxa sheyga waxyeelada leh. Daaweynta weecasho ka dhigan tahay in uu bedelay dabiiciga ah, laakiin filtarka burburay, macmal ah qalliin.

Marka koraya iin

Tani waxay ifafaale bahal ah (nooc kasta) waxaa inta badan la sameeyay inta lagu guda jiro SNMna morphogenesis (ie, 3-10 toddobaad). Dhab ahaantii Tan waxa u sabab xaqiiqada ah in waqtigan, xadgudbay nidaamka dhalmo, kaladuwan, socdaalka iyo dhimashada unugyada. ifafaale dhacaan heerarka dheecaanka, intracellular, mezhorgannom, extracellular, xubnaha iyo unugyada interstitial.

noocyada hadda jira ee

Congenital - waa qaybta ballaaran, oo ay ku jiraan xaaladaha aad u kala duwan ka cillado jir ahaaneed yar (tusaale ahaan, jiirarka waaweyn, birthmarks, iwm ..) Si xadgudubyo halis ah ee nidaamyada shaqsi (tusaale ahaan, iin wadnaha waalka, cilladaha Addinka, iyo wixii la mid ah.). Sidoo kale waxaa jira aan caadi ahayn isku dhafan oo saameeya qaybo badan oo jidhka ah isku mar. Cilladaha in dheef sidoo kale loo arkaa dhasho.

In dhaqanka caafimaad, waxaa jira saddex nooc oo aasaasi ah cilladaha lagu dhasho:

  • khaladaadka ku diiso-shiid,
  • cillad-jirka ah ee lagu dhasho,
  • cillado kale ee hidaha.

noqnoqoshada dhacdo

waxbarashada muddada dheer ee cillado lagu dhasho ayaa muujiyey in mid ka mid ah ama khalad kale ee ilmaha caloosha ku muuqataa at inta jeer gaar ah, taas oo ku xidhan jinsiga uu ilmuhu. Tusaale ahaan, stop clavate iyo stenosis pyloric waa caam ku tahay wiilasha, iyo barakacyo hip lagu dhasho - in gabdhaha.

Ka mid ah kuwa carruurta ku dhalatay mid ka mid ah kelyaha, iyo wakiillo ka badan oo jinsi xoog. Sidoo kale waa in la ogaadaa in badan oo cillado kuwan, sida tirada badan feeraha, ilkaha, araxda iyo xubnaha kale, waxaa laga helaa ka mid ah gabdhaha dhasha.

List of curyaanimo

Maanta, waxaa jira cilado badan. Inta badan waxay la ogaado inta lagu jiro cilmi hooyadiis ultrasound ee ah. Haddii yaab leh filan u daran yahay, naag ku bixiyey in la joojiyo uurka. Tan waxa u sabab ugu horrayn si ay xaqiiqada ah in ilmaha dhalan doonaa nolosha oo dhan halis, iyo dareento liita (ku xiran tahay nooca aan caadi ahayn).

Aynu wada fiiriyaa waxa curyaanimo jiro:

  • iin aortic;
  • atresia of jejunum ah ;
  • iskaanka of sambabada;
  • acrania;
  • iskaanka kelyaha laba geesoodka ah,
  • Anencephaly;
  • aamadii lagu dhasho ee sinta;
  • iskaanka kelyaha gooni;
  • atresia esophageal;
  • cloaca dhasho;
  • albinism;
  • Ururka VACTERL;
  • aplasia of sambabada;
  • dhanxanegga dillaacii;
  • atresia dabada,
  • stop clavate;
  • Downs syndrom ,
  • cretinism dhasho;
  • megacolon dhasho;
  • cudurka wadnaha lagu dhasho,
  • yiraahdo hydrocephalus;
  • Sheelada,
  • hypoplasia of sambabada;
  • diverticulum esophageal;
  • syndactyly;
  • polysomes by X-koromosoomyada,
  • diverticulum Meckel ee;
  • Patau syndrome ,
  • dibinta dillaacii;
  • polysolid;
  • Klinefelter ee syndrome,
  • cryptorchidism;
  • cilladaha xubnaha galmada;
  • clubfoot;
  • Klippel-Feil syndrome,
  • megacolon;
  • CRI du chat,
  • microcephaly;
  • Turner ayaa syndrome,
  • hypoplasia ee lafta bawdada iyo soo gaaray lafaha,
  • syndrome uurjiifka khamriga;
  • omphalocele;
  • Sheelada spinal,
  • fibrodisplations;
  • stenosis pyloric;
  • polydactyly;
  • Edwards syndrome ,
  • synophtalmia;
  • exencephalocele;
  • exstrophy kaadi haysta,
  • epispadias;
  • ectrodactyly.

Si Loo soo kobo

Sida aad arki karto, waxaa jira wax badan oo ka mid ah cilladaha lagu dhasho kuwaas oo ka dhaca caloosha ku horumarka utero. Si looga fogaado dhacdo ee aan caadi ahayn sida in waalidiinta mustaqbalka ilmahooda waa inay iska ilaaliyaan soo-gaadhista arrimaha qayb waxbarashadooda. Sayidka, hooyooyinka iyo aabayaasha mustaqbalka, waxaa lagu talinayaa in la siiyo ilaa cabbo khamri 6-9 bilood ka hor rimidda, oo aan la isticmaalayn xilliga uurka (dumarka). Intaa waxaa dheer, waa in aad joojiso sigaarka, ka fogaadaan meelaha ay waxaa laga yaabaa in shucaaca ionizing, ha qaadan daroogo, aan qoray dhakhtarka marar badan in ay dibadda u noqon oo ay qaadaan dhamaan fitamiin iyo macdan lagama maarmaan.

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