Caafimaadka, Daawo
Cudur, shalalka waa purpura thrombocytopenic
Waayo, markii ugu horeysay ah, shalalka purpura thrombocytopenic, waxaa lagu tilmaamay in 1735, purpura thrombocytopenic, cudur lagu arkay gabar toban-sano ah. Currently hoos foomka magacan la isku daray, shalalka Torombositobiiniya, sababta autoaggression at kaas oo ku guuldareysto. Waxay u muuqdaan diathesis hemorrhagic la deficiency go'doon ah platelets. Qoondee qaab daran ama dabadheeraad ah cudurka.
sababaha
purpura thrombocytopenic Ba'an inta badan ku xanuunsado oo carruur ay da'doodu 2 ilaa 9 sano. purpura Thrombocytopenic ee carruurta waxa lagu gartaa bilawga lama filaan ah oo dib u soo kabashada degdeg ah. Horumarinta ee daliilka kiliinikada inta badan kor u caabuq fayras ee aagga sare ee neefsashada ama shiidka. In 10% ee kiisaska cudurka la xidhiidha horumarinta virus varicella, virus Epstein-Barr, tallaalka, immunotherapy BCG. burburinta dhiig xinjirowga ay sabab u tahay wax ka qabashada difaaca jirka ee u shaqeeyo halkii tallaabo ah ee fayraska.
Foomamka Chronic of Torombositobiiniya mudo ka badan 6 bilood waxaa lagu magacaabaa purpura thrombocytopenic idiopathic. Sababta oo ah cudur aan la garanayn. Thrombocytopenic purpura inta badan bilaabaa in ay qaan, baaluq. Badanaaba ku badan dumarka.
daliilka Clinical si tartiib tartiib ah u muuqdaan. Lagu gartaa dabcan daba-soo noqnoqda ama sii dheeraaday cudurka. salaysan Pathogenetic cudurka waxaa la adkeeyo oo la dedejiyey burburinta dhiig xinjirowga by autoantibodies iyaga ka gees ah.
sawir clinical
On maqaarka ee bukaanka qaba calaamadaha microcirculatory nooca dhiigbaxa sida punctate finan petechial hematoma subcutaneous yar, purpura on xuubka afka. Lagu gartaa dhiig ee xub-axaleedka of sanka, ciridka. Isbedelada oo dubka inta badan waxay ku yaalaan on dusha hore ee jirka jirridda, sare iyo hoose. Sida caadiga ah formation of hemorrhage waaweyn ee goobaha la duray. Mararka qaarkood waxaa laga yaabaa in dhiig gelin sclera iyo ileyska, dhiigbaxa marinka dheef shiidka. In dumarka, waxaa jira hemorrhages ee ugxan. In noocyada halista ah ee dhiig cudurka kelyaha laga yaabaa inuu dhaco.
purpura Thrombocytopenic waxay keeni kartaa dhibaatooyin khatar ah sida hemorrhage cerebral iyo subarachnoid hemorrhage. Dabeecad wanaagsan waa cabbire imtixaanka-Konchalovsky beerfale-LEED: formation of hemorrhages meelaha maqaarka ah riixo. qanjidhada, beerka iyo caajisnimo ma ballaadhisay.
Baadhista xanuunada
feature ugu weyn ee shaybaarka waa in la yareeyo tirada platelets. waqtiga xinjirowga dhiigga aan la xadgudbay. Heparin plasma ayaa kor u kacay. Marar badan, go'aamiyo kordhinta ee immunoglobulin G platelets. Ka dib markii dhiig la taaban karo lagu qeexay anemia dhiigbaxa ba'an.
daaweynta
Haddii la purpura thrombocytopenic cudurka, bukaanada la bilaabo daweynta corticosteroids. Inta lagu jiro daaweynta, bukaanka lagu arkay koror joogto ah ee dhiig xinjirowga ku tirinay ilaa dembidhaafka dhamaystiran. la'aanta ah ee waxtarka corticosteroids oo immunomodulators qoray delagil. Iyada oo waxtardarradoodu ee therapy muxaafidka ah 6 bilood gudahood ku talinaynaa fulinta splenectomy.
Dhinac kale oo therapy - maamulka qaadasho sare ee immunoglobulin duro xididka muddo 5 maalmood ah. diyaarinta Kuwani daawaca antibodies in xidhxidhaan iyo ka saari viral, bakteeriyada iyo kale cudur.
In 80-90% bukaannada ku jira dib u soo kabashada lama filaan ah waxay dhacdaa 1-4 bilood gudahood. Xaaladaha qaarkood, purpura thrombocytopenic socon karaa ilaa 12 bilood. Cudurku waa mid noqoshada joogto ah: dhiig caadada beddelayaan caadada ah dembidhaafka.
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