Felty ee Syndrome: Calaamadaha, Diagnosis

Under Felty ee syndrome loola jeedaa dhibaatooyin of rheumatoid arthritis, taas oo dhacda in% dhamaan bukaanka qaba cudurka 1 keliya. Qandho, atrophy muruqa, midabka iyo nuglaato in dabeecadda cudurada faafa - dhammaan arrimahaasi waxay sida caadiga ah la socon Felty ee syndrome. Pathology Baaritaanka ku salaysan tahay taariikh rheumatoid arthritis, muhiim u sugnaaday xuduudaheedu shaybaarka. Daaweynta ku lug leedahay qaadashada of corticosteroids, splenectomy. Muddo dheer cudurada a gartaa nooca aan la hubin iyo sawir caafimaad. In 1929, AP Felty tilmaamay cudurka. Ever tan iyo markii cudur la kala sidii nosology madax banaan.

Felty syndrome: waa maxay?

Cudurku waxaa lagu qeexaa by joogitaanka saddex heley wadajira: arthritis ah rheumatoid, caajisnimo la weyneyn iyo leucopenia (unugyada dhiiga cad ku yar). syndrome Tan waxaa badanaa la ogaadaa in dadka ka weyn 40 sano, sida caadiga ah ee jinsiga cadaalad ah.

Khubarada ayaa soo jeedinaya in sal u ah cudurka waxa weeye geedi socod, shalalka. Waxa soo baxa la qaybqaadashada tooska ah ee unugyada lymphoid iyo formation xiga ee kaxeynayo difaaca iyo sidoo kale antibodies gaar ah. Pathology muujiyey sida neutropenia la hoos khasab ah in iska caabin ah in cudurada ugu badan, iyo marka ay dhacdo - si aad u daran. Maanta waa splenectomy (bixinta caajisnimo ah) waxaa loo aqoonsan yahay habka kaliya wax ku ool ah ee daaweynta.

Felty ee syndrome waxa lagu gartaa kala duwanaanshaha weyn, inta badan atypical. Meejeeda hor waxaa laga yaabaa in dhowr sano (5 ilaa 10) cudurada wax-u polyarthritis rheumatoid la lug isku mar ku jira laabatooyinka interphalangeal habka bahal ah, oo leh heerar kala duwan ee darnaanta.

Dhinaca kale, inta badan ee bukaannada qaba cudurka this waxaa go'aamiya daliilka caadiga ah ee unugyo. Tani waxay noqon kartaa qandho, formation of qanjira subcutaneous, myocarditis, khasaare ah oo miisaankeedu yahay, poliserozita.

Sababaha ugu waaweyn

etiology cudurka waa la garanayn. oo dhan bukaanka qaba cudurka ah "rheumatoid arthritis" aan la soo koraya cudurada this. In dhuuxa lafta qofka caafimaad waxaa si joogto ah soo saaray unugyada dhiiga cad. Bukaanka qaba this syndrome, inkastoo wareegga a yar, leukocytes ayaa sidoo kale sameeyay. Waxay ku ururto laga yaabaa in qadar xad-dhaaf ah ee beeryarada.

Waa maxay calaamadaha weheliyay Felty ee syndrome ee dadka waaweyn?

• syndrome Articular (arthritis oo ka mid ah kala-goysyada yar).
• Kordhinta size ee beerka.
• Lymphadenopathy guud (ogaadaa in 50% ee kiisaska).
• Kororka horusocod ah ee size caajisnimo (sida uu go'aamiyo taataabasho).
• Polyneuropathy.
• Midabka maqaarka, nabaro in ka Faydatay Dhudhumadeeda ah.
• Waajihi fibrosis pulmonary.
• qanjira rheumatoid.

Dhamaan sifooyinka kor ku xusan ka dhigi suurto gal ah si loo baadho Felty ee syndrome. Calaamadaha bukaanka oo dhan waxaa lagu muujiyey duwan. Tusaale ahaan, mararka qaarkood wayneeyo of caajisnimo ah ayaa lagu arkay oo keliya ee marxaladaha ugu dambeeya ee horumarinta cudurka.

cudurka

The saldhig u ansixiyo kama dambaysta ah ee cudurka caafimaad ee isku darka isku mar ah splenomegaly iyo rheumatoid arthritis. baaritaanka dhiigga waxaa lagu gartaa dhiig, leukopenia, neutropenia. immunoassay caadi ahaan lagu ogaadaa titers sare RF, CEC ah, jiritaanka unugyada antinuclear. Sida ay natiijada Dabanicista kelyaha dhuuxa myeloid laga helo wareeg ah xagga xubno gacanta qaan gaadhin. Hababka Qalabka baaritaanka (MRI, CT, ultrasound kalagoysyada) ay u badan tahay inuu bixiyo macluumaadka yar. Felty ee syndrome waa mid aad u muhiim ah in la kala saaro oo la cirrhosis iyo sarcoidosis.

mabaadiida aasaasiga ah ee daaweynta

Therapy, haddii ay taasi ku lug leedahay in hab ballaaran. Rheumatoid arthritis waxaa lagu daaweeyaa sida caadiga ah. Therapy noqnoqda cudurada, iyo arthritis oo ay ku jiraan dawooyinka ka caawiya laabotooyinka ( "azathioprine", "MTX").

Bukaanka qaba caabuqyada halista ah waxaa lagu talinayaa in ay sameeyaan irbado todobaadle ah factor, oo wuxuu kobciyaa gumeysi granulocyte. Waxa uu kordhiyaa tirada unugyada dhiiga cad.

daawooyinka aasaasiga ah waxay yareyn kartaa symptomatology kaas oo si toos ah u raaci arthritis, Felty syndrome. waxaa ka mid ah waxaa ka mid ah: "Daawada methotrexate", "Penicillamine".

Glucocorticoids waa wax ku ool ah oo kaliya in qaadashada sare. Haddii kale, waxaa sii kordhaya suurtagalnimada ee soo noqoshada. Dhinaca kale, isticmaalka daba dheeraaday ee glucocorticoids waxay keeni kartaa in horumarka cudurada intercurrent.

Shuruudaha for waxtarka therapy:

• Kordhinta tirada granulocytter 2000 / mm.
• Dhimista ee dhacdooyinka dhibaatooyin faafa ee dabiiciga ah.
• Dhimista weeraro qandho.
• Dhimista of boogaha on daliilka maqaarka.

Marka qaliin lagu talinayaa?

Sidee kale oo wax idinka Adkaan oo Felty ee syndrome? Daaweynta by qaliin lagu talinayaa haddii daaweynta daroogada ahaa weydo ama sababta oo ah sabab kasta, waxa waa u. Xaaladdan oo kale, sida caadiga ah waa su'aal ah splenectomy. Waxaa muhiim ah in la xasuusto in in 25% ka mid ah xaaladaha of neutropenia gow ah ka dib hawl this.

Under splenectomy macnaheedu qaliin, intii lagu jiray taas oo dhakhtarku si buuxda ama qayb ahaan ka saaraysaa caajisnimo ah. Maanta, waxaa jira laba fursadaha nidaamka noocan oo kale ah: splenectomy laparoscopic oo furan.

Laparoscopy waxaa la sameeyaa iyadoo la isticmaalayo suuxin guud. Xaaladdan oo kale, howlgal ay ku lug leedahay codsiga of qalab khafiif ah la camera a on dhamaadka, oo la yidhaahdo laparoscope ah. Dhakhtar ka dhigayaa jeexitaano yaryar oo dhawr caloosha kaas oo barayaa qalab loogu talagalay manipulations xiga. muddo dib u soo kabashada, sida caadiga ah, uma baahna waqti badan.

splenectomy Open ku lug leedahay la qalay weyn hoos ugu feeraha, kaas oo qalliinka ka saaraan caajisnimo ah. Ka dib saarista ee jirka awooda jirka ee ka miiro bakteeriyada iyo fayraska dhiigga waxaa muuqata hoos.

dhibaatooyin ay suuragal tahay

Dhibaatooyinka waa cudur aad u dhif ah oo u muuqdo waxaa laga yaabaa in qaab beeryaro dhaawacmay, horumarinta wax-u hypertension portal, caloosha iyo mindhicirka dhiig si dhib leh ku dhaco cudurada sare.

gunaanad

Felty ee syndrome - cudur dhif, laakiin halkii dhibaato ka mid ah koox dhan oo heley oo maanta dhif ah laga helay. Tani macnaheedu ma aha in aan dayicin karaa daaweynta iyo ma in ay raadsadaan caawimo aqoon dhakhtarka ku haboon. calaamadaha Primary feejignaan qof walba oo ay noqoto sabab talo ku takhasusay doonaya. Haddii kale, waxaa sii kordhaya fursadaha ka sii daraysa ee gobolka guud iyo horumarka ku filan halista dhibaatooyin caafimaad, oo ay ka mid dillaac of caajisnimo laftiisa. Doorashada wax ku ool ah oo kaliya daaweynta Hadda waxaa la aqoonsaday sida splenectomy ah.

Waxaan rajaynaynaa in dhamaan macluumaadka lagu siiyey in this article on topic noqon lahaa runtii waxtar kuu. Joog caafimaad!