CaafimaadkaCaafimaadka Ragga

Hypogonadism ragga: Calaamadaha iyo Daaweynta

hawlgalka Full nin ee jirka oo aan la malayn karo iyada oo aan shaqaynaya saxda ah ee qanjidhada jinsi, wax soo saarka ee hormoonnada. failure kasta ee nidaamka this wuxu ah ee cudurada degaaankaaga. Dyslipidemia, atherosclerosis, cayilka, ischemia maskaxda - tani ma aha liiska oo dhan ee dhibaatooyinka ay suurtagal tahay. In buugaagta tixraaca caafimaad helay sharaxyo badan oo xadgudub sida. Tusaale ahaan, deficiency antiandrogen Testicular ama daawo. Si kastaba ha ahaatee, iyaga ka mid ah, ugu daacadsan oo ugu sax ah loo tixgeliyaa in ereyga "hypogonadism" ee ragga. In xaaladan ay tilmaamaysaa, sabab kasta ha sara joogsado haddii ay waxaa lagu daawayn karaa - su'aalahan waxaa lagu soo bandhigay jawaabo faahfaahsan ee article maanta.

Sharaxaad kooban oo ka mid ah cudurka

Hypogonadism - cudur lagu gartaa ah qanjidhada functional galmada deficiency. The wakiilada jinsi xoog waxaa lagu soo bandhigay xiniin midig iyo bidix. Nature ayaa la siiyaa sidii tiradoodu ay si gaar ah u aadeen. dareen unugyada Xiniinyaha in khataraha deegaanka kala duwan. In case of luma kartida functional ee jirka waa in ay haystaan nooc ka mid ah reserve. awoodda Regenerative ee xiniinyaha waa arrin suubban.

Ay ujeedada ugu weyn ee - in ay faafin. La'aanta awooda in uu soo saaro manida u diidaa jirka ka mid ah awoodaha taranka labka ah. Farsamo xadgudubyada sida marxalad hore ee wareegga taranka dhigay. Sidaa darteed, dhalmo la'aan, horumarinta ku saabsan asalka this, waxaa loo arkaa mid aad u halis ah. function soo celi of unugyada aan caadiga ahayn ee unugyada Testicular waa ku dhowaad aan macquul ahayn.

Hypogonadism in rag lagu gartaa sifooyinka soo socda:

  • hoos u si tartiib ah in heerka hormoonnada jinsiga,
  • hoos ka mid ah sifooyinka oo tayo iyo tiroba mid ah manida,
  • hypoplasia ee xubnaha taranka,
  • xanuunada hormoon jidhka oo dhan.

Sida laga soo xigtay tirakoob, syndrome ee hypogonadism in rag ku dhacdaa 1% ka mid ah dadka dunida ku. Si kastaba ha ahaatee, macluumaad this waa meel gaarka ah, sida xisaabta lagu daro oo keliya xaaladaha diiwaan gashan ee cudurada. Daaweynta daruuri fuliyay iyada oo ay kormeerayaan endocrinologist iyo andrologist. The therapy hormone inta badan la isticmaalo. Marka loo xilsaaray waxtardarradoodu qalliinka caag ah iyo aalka xubnaha habka taranka.

Sababaha ugu waaweyn ee cudurka

horumarinta hannaanka bahal qaadataa meel ay sabab u tahay yaraynta tirada hormoonnada soo saaray ama biosynthesis disorder. By arrimo etiological cudurka waxa ka mid ah:

  • curyaanimo lagu dhasho ay keento isbeddel ah ee qaab dhismeedka Testicular iyo / ama tubules seminiferous;
  • saameyn ku shaqeeyo sunta hooyooyinka mustaqbalka (khamriga, nikotiinka, daroogada);
  • mari shucaaca ama chemotherapy;
  • isticmaalka muddada-dheer ee hormoon, daawooyin lid ku ah bakteeriyada,
  • cudurada faafa ee asal ahaan (orchitis ka dib markii jadeecada, qaamo-qashiir, kiishka);
  • Xidido Dhiig oo ah xiniinyaha,
  • hoy meelaha xaaladaha deegaanka loo kasin.

Sababaha hypogonadism ragga keeni qaabka geedi socodka bahal ah. Mid kasta oo iyaga ka mid ah waxa lagu gartaa maris gaar ah.

xadgudubyada kala duwan

Iyadoo ku xiran sababta dahsoon ee dhacdo of gonads failure qaybsan da'da hoose, sare, iyo kuwa lagu magacaabo. Sidee bay u kala duwan yihiin? Foomka waxaa aasaasiga ah ee cudurka waa si kale loo yaqaan cudurada Testicular. Xaaladdan oo kale, u dhexaysay ee xiniinyaha shaqeeyaan socday sarkhaansan arrimood negative dibadda. hypogonadism Secondary in rag waxa uu la xidhiidhaa aan caadi ahayn in nidaamka "pituitary-hypothalamus". Nidaamkan soo saaray hormoonnada masuul ka ah hawlaha ee xiniinyaha. duwanaansho Age of cudurka waxaa loo arkaa inay nooc ka mid ah dayska lab. sababaha, dhakhaatiir ma sharxi karaan ilaa maantadan la joogo.

kala soocidda soo socda ku xiran tahay xiliga nolosha, taas oo waxaa jiray cudur. Foomka embriyaha waxaa lagu gartaa muuqaalka kore ee geedi socodka a bahal ah ee muddada horumarinta, makaanka. Prepubertal cudurka ka hor qaangaadhnimada (14 sano). muuqashadii Postpubertatnom cudurka dhacdaa marka la dhameystiro ee horumarka ah tilmaamaha galmada sare.

Marka la eego xaddiga androgens soo saaray, la kala saaro ah noocyada soo socda ee cudurka:

  1. hypogonadism Hypergonadotrophic. In ragga, foomkan cudurka muuqato qaab burburka unugyada Testicular Testicular. Waxa ay la socotaa wax soo saarka kor u kacay hormoonnada pituitary. At tilmaamayaasha waqti isku mid ah testosterone si weyn u dhimay.
  2. hypogonadism Hypogonadotropic. Waxaa lagu gartaa Avv hoos u of gonadotrophins. Tani waxa ay yaraynaysaa qadarka testosterone soo saaray.
  3. hypogonadism Normogonadotropic. In ragga, foomkan ee geedi socodka bahal keenaysaa in carqalad ah xiniinyaha, laakiin wax soo saarka ee hormoonnada pituitary waa caadi. Cudurku wuxuu inta badan la xidhiidha cayilka.

Iyada oo ku xidhan etiology waa caado ah in la kala saaro foomamka lagu dhasho, helay iyo idiopathic. Xaalada danbe, sababta ugu weyn ee cudurka ayaa weli aan la garanayn.

hypogonadism hoose

Cudurku wuxuu noqon karaa mid labada helay oo lagu dhasho. Inta badan, cudurada ku dhacdaa utero. Boy dhashay guska yar iyo xiniinyaha ah dhacsan. Sida horumarka ee sawirka caafimaad ee mutates cudurka. In wiilasha qaan la cayilan, daliilka hore gynecomastia cudurka la ogaado iyo heerka hoose ee timaha jirka.

Acquired hypogonadism aasaasiga ah ee dadka oo horumarisa bararka oo ka mid ah qanjidhada ku taalba hoos cudurada soo socda:

  • orchitis;
  • kiishka;
  • epididymitis;
  • mumps,
  • busbuska.

Qaabkan cudurka waxaa loo arkaa inay ugu badan. Waxay dhacdaa in mid ka mid ah shan nin oo hore cudurka dhalays.

hypogonadism Secondary

hypogonadism Sare waxaa laga yaabaa in lagu dhasho ama heleen. In kiiska ugu horeeya ee cudurka waxaa ka hormarey horumarinta dheecaan aan habboonayn ee pituitary iyo hormoonnada hypothalamic. Waxaa inta badan la socda oo hiddo:

  • Prader syndrome - Willie;
  • syndrome Maddock;
  • syndrome Pasqualini.

Foomka waxaa helay cudurka inta badan sababa caabuq xuubabka maskaxda. iyaga ka mid ah waa meningitis, arachnoiditis iyo encephalitis.

Calaamadaha cudurka carruurta yaryar

Sawirka caafimaad ee geedi socodka bahal ah waxaa inta badan lagu go'aamiyaa da'da bukaanka. Its horumarinta ka da'da hore waxaa badanaa la socdo calaamadaha soo socda:

  • Disorder baaluqo
  • muuqaalka evnuhoidizma calaamadaha (koritaanka xad-dhaafka ah sare, garbaha yar, addimada dheer);
  • maqnaanshaha qabsatay in Xiniinyaha;
  • size yar ee guska,
  • gynecomastia.

In joogitaanka mid ama ka badan calaamadaha kor ku xusan waa in isla markiiba la tasho khabiir profile ah.

Calaamadaha cudurka ee dhallinyarada

horumarinta cudurka in ay qaan waxa lagu gartaa calaamado la mid ah, prepubertal in. sawir Clinical buuxsan kartaa hoos libido iyo xad dhaaf ah. Si aad u aragto takhtar waxaa sida caadiga ah ogaan hypoadrenalism iyo thyroid. Dusha, dhallinyarada bukaanada si cad u muujiyey horumar nidaamka muruqa ah.

Calaamadaha cudurka ee dadka waaweyn

Hypogonadism ragga ka weyn yahay 30 sano ka yar fahmayaan. cudurka waxaa la socda muuqaalka kore ee laalaabka badan baruurta jidhka ka mid ah. Maqaarka muddo lumin barti hore oo engegi. Waxay u muuqataa daal, lability dareenka, u janjeera in la niyad-jabka. Nasiib darro, isbitaalka loola dhaqmo by rag xaalado gaar ah. Sida caadiga ah marka ay timaado dhalmo la'aan ama xanuunada function kacsi.

Tani la'aanta fiiro gaar ah u caafimaadkooda keeni kartaa cawaaqib xun. Geedi socodka bahal bilaabaa inuu ku faafay ma aha oo kaliya on habka taranka, laakiin waxaa si tartiib ah u dhaqaaqo xubnaha kale iyo unugyada. Maqnaanshaha daryeelka karti u horseedi karaa naafada.

hababka ogaanshaha

Ha baqin ee cudurka Dhicis hypogonadism ragga. Taasi gobolka taasi ka dhigan tahay inaad u sheegto dhakhtarka ee tashi ugu horeysay. Ka dib markii muuqaalka kore ee calaamadaha cudurka waa in isla markiiba la xiriir farsamo aqoon. Inkastoo sawirka si caddaalad ah oo dhalaalaya clinical, waayo xaqiijin cudurka u baahan tahay inaad ku mari qiimaynta kiliinikada. Waxaa ka mid ah hawlaha soo socda:

  • baaritaan jireed;
  • ultrasound miskaha;
  • karyotype;
  • urinalysis;
  • shahwada,
  • baaritaanka dhiigga hormoonada.

Baaritaanka waxaa loo xilsaaray in bukaan kasta si gaar ah. Sidaa darteed, liiska dhacdooyinka caafimaad oo laga yaabaa in wax yar ku kala duwan yihiin. dhakhtarkaaga ayaa xaqiijiyay ama beeniyey cudurka hordhac ah oo ku saleysan natiijooyinka helay, meelaynayaa therapy.

Features ee daaweynta

Selection of hab gaar ah ee daaweynta waa in ay dhakhtarka iyo waxaa ka go'an iyada oo la tixgelinayo sababaha cudurka. daaweynta hypogonadism ragga sida caadiga ah waxa uu leeyahay dhowr gool: cudurada ugu waaweyn ee la dagaallanka, ka hortagga dhalmo la'aan, ka-hortagga ah ee dhacdo of burooyinka in nudaha Testicular.

Foomamka lagu dhasho iyo prepubertal of cudurada waxaa inta badan la socda dhalmo la'aan. Baabi'iyo dhibaatadan suurtogal ma aha. Haddii endocrinocytes kaydiyaa xiniinyaha, waxaa lagu talinayaa therapy kicinta. Carruurta qoro daawooyinka hormoonnada ah, iyo dadka waaweyn - waa androgens. Maqnaanshaha hormoonnada hormoonada jidhka u baahan tahay in aad cabto nolosha oo dhan.

In foomka sare gonadotropic habka bahal qoray daroogada ee qiyaasta yar. Haddii loo baahdo, ay weheliso testosterone. doorka A ee lagu daaweeyo cudurka iska leh jimicsi oo aad hesho kaxeynayo vitamin.

Dhammaan daawooyinka loo qoro si gaar ah ku xiran tahay xaaladda caafimaad iyo da 'bukaanka. isticmaalka daaweyn beddelaad ah oo leh wakiilada hormoon laguma talinayo in xaaladaha qaarkood. Tusaale ahaan, in lesions kansarka qanjidhka. weerar Chronic cudurada sanbabada, sigaarka, shiid baruurta oo yaraada iyo xibin gal - yihiin sababo qaraabo. Xaaladan oo kale, go'aanka oggolaanshaha ee daroogada testosterone si gaar ah loo qaaday.

qalliin

Haddii hypogonadism ragga waxaa keena itaaldarrida jirka iyo horumarinta ee xubnaha taranka, oo muujinaya hawlgalka. Maanta, noocyo kala duwan oo doorasho ee faragelinta loo isticmaalaa in lagu baabi'iyo cudurka. Tusaale ahaan, la hypoplasia guska waxaa loo isticmaalaa phalloplasty, in ay dhacdo testis undescended waxaa la sameeyaa heerka labaad. ku rakibida testis dardaro qaadeen in la baabi'iyo khaladka la isku qurxiyo. Mid ka mid ah hawlaha kuwan waxaa la sameeyaa iyadoo la isticmaalayo farsamooyin microsurgical.

Saadaasha rayshada

hypogonadism Hoose, gaar ahaan dhasho, waxaa lagu sixi karaa qayb ahaan. Waxaa ku saabsan soo celinta awoodda jidh iyo functional guska waa. Si kastaba ha ahaatee, daawo casri ah si caadi Shahwada ma aan samayn karo. Fursada kaliya in ay dib dhalmo - shahwada IVF iyada oo deedka ku. Sayidka spermatogenesis vnutriyaichkovy waa in lagu hayaa.

Saadaasha kale filanaya in bukaanka cudurka hypogonadism sare. In ragga, daaweynta cudurka kiisaska intooda badan ku siin natiijo fiican. Sidaa darteed, dhakhaatiirta inta badan ma soo celin karo dhalmadii.

tallaabooyinka ka hortagga

ka hortagga gaar ah oo cudurkan aan la horumariyo. Waxaa ka mid ah talooyinka guud ee dhakhaatiirta wac kuwa soo socda:

  • daaweyn degdeg ah cudur kasta,
  • nafaqo sax ah, la'aanta caadooyinka xun, jimicsi,
  • marayay kormeerka ee dhakhaatiirta "lab" qiyaas ka hortag ah hal mar sannadkii.

talooyinkan, nasiib darro, ma aha had iyo jeer suurto gal ah si looga hortago in hypogonadism ragga. At koowaad ee daliilka ay tahay in si degdeg ah kaalmo ka takhasus u doondoonto. The daawaynta Dhakhtarkaaga ayaa kuu qori hore, ee si degdeg doono habka bogsashada.

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