CaafimaadkaDaawo

Amyloidosis kelyaha: foomamka, astaamaha iyo daweynta

Waxaa jira noocyo kala duwan oo ka mid ah cudurrada kelyaha. Mid ka mid ah waa amyloidosis taas oo dhigaalka amyloid ah in unugyada. Amyloid laga sameeyey xanuunada shiid iyo waa xarunta adag ee borotiinada iyo polysaccharides. amyloidosis kelyaha ayaa dhawr foom oo waaweyn:

1. Primary (taas oo weli waxbay ushafeeci idanka magaca amyloidosis idiopathic iyo genuinnogo), taas oo sabab u muuqata waa ay adag tahay in la qeexo.

2. sare, taas oo dhacda ku saabsan asalka ah cudurada raaga.

3. A hidde (dhaxlo, qoyska), kaas oo soo baxdo natiijo ahaan xanuunada hidaha ee Avv borotiinka.

4. neefo

Sida dhaqanka shows, amyloidosis sare kelyaha waa ka caadi hoose. Xaaladdan oo kale, caabuq sababa in ay dhacdo, waxay noqon kartaa kala duwan. Waxay qaadi karaan oo sabab u ah cudurka qaaxada, osteomyelitis, iyo sidoo kale cudurada la xiriira suppuration pulmonary. Sidoo kale, foomkan cudurka u muuqataa in rheumatoid arthritis, ulcerös kolit. Marar dhif ah, amyloidosis kelyaha dhici karaan dhanka ah asalka ah hogaga, qumanka, naaso, iyo waraabow.

Sida caadiga ah, amyloidosis kelyaha, calaamadaha laga yaabaa in aanay muuqan, ayaa dhowr sifooyinka aasaasiga ah oo macquul ah:

1. Muuqashada barara

2. tabar wakhtiyeysan

3. Shuban

4. Cadaadis dhiig oo sarreeya

5. failure Kelyaha

Joogitaanka borotiin laga helo kaadida - muujinta a caan ku dhammaan noocyada amyloidosis. amyloidosis kelyaha keenaysaa in carqalad ah wadnaha iyo mareenka caloosha iyo mindhicirka. Sida caadiga ah, Baadida garaaca wadnaha oo deggan iyo dhacdaa wadnaha. Weli waxaa jira beerka balaartay iyo beeryarada, inkastoo calaamadaha dhalaalaya oo ay ka shaqeynayaan ma muuqdo laga yaabaa.

Si loo ogaado amyloidosis kelyaha, loo baahan yahay si ay u qabtaan biopsy a of kelyaha, beerka, colon iyo maqaarka. Sida caadiga ah, biopsy a galkii malawadka in ka badan 70% ka mid ah xaaladaha ka caawisaa in la ogaado amyloid. Dhakhaatiirta sida caadiga ah ugu kalsoon tahay biopsy.

Amyloidosis ayaa sidoo kale fuliyay echocardiography, taas oo muujin kartaa shaabadda derbiga ventricle bidix, septum dhexeeya intraventricular ah, iyo sidoo kale calaamadaha function diastolic oo yaraada. Sida caadiga ah, in cudurkan uu ka tagay tirada qolkii ventricular ee caadiga ah ama la dhimay. Marka ultrasound ayaa la fuliyaa, dhinacyada kelyaha sidaas hadyada meejeeda, waxaa laga yaabaa in si caadi ah ama kor u kacay.

daawo Modern ma laha daaweyn gaar ah cudurada sida amyloidosis kelyaha. daaweynta, oo caadi ahaan lagu, waxaa loogu talagalay ugu horeyn at baabi'inta sababaha keena in horumarka cudurka (waxay khuseysaa Mararka ay amyloidosis waa sare) ah. Sida caadiga ah, qofka bukaanka ah waxaa lagula talinayaa in cunto gaar ah iyo saf ah chemotherapy. Mararka qaarkood kelyaha iyo kelyaha beerista, taasoo badalay xubnaha ka buka.

Haddii amyloids ku yaalaan kasta oo ka mid ah xubnaha ama faafin jirka oo dhan, amyloidosis ma aha mid halis u ah nolosha bukaanka. Calaamadaha cudurka ay sahlan tahay. Haddii kale, waxay ku xiran tahay dib u soo kabashada therapy si fiican u doortay, xoogga daaweynta iyo darnaanta cudurka in uu keeno horumarinta amyloidosis.

ammaanka Health si looga hortago horumarinta cudurka. Sida caadiga ah, ka-hortagga waa daaweynta waqtiga cudurka, taasoo keeni karta dhaawac kelyaha iyo horumarinta amyloidosis. Ujeedada this waxaa lagama maarmaan ah si uu tijaabada baaritaanka caafimaad oo joogto ah iyo in ay qaataan imtixaanada loo baahdo. Markaas halista ah inay sii xumaanayso oo dhacdo ee cudurka waxaa si weyn u dhimay.

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