Astaamaha la xidhiidha hemolytic-uremiskt syndrom iyo sida loo daweeyo

Sidaas daraaddeed, waxa aad u baahan tahay ugu horreeya oo dhan in la ogaado ay sabab u tahay syndrome ee hemolytic-uremiskt (loo soo gaabiyo - HUS). Dhakhaatiirta u yeelaan cudurkan inta badan saddex calaamadaha: kelyaha ee daran, dhiig hemolytic, Torombositobiiniya. Waa in la ogaadaa in feature dambe waxaa sida caadiga ah ugu si cad u muujiyey. Cudurku waxaa lagu ogaada ayado ugu horayn in carruurta yar yar.

sababaha suuragalka

Sababaha ugu weyn ee la xidhiidha hemolytic-uremiskt syndrom - dareen xaasaasi ah in daawada, iyo sidoo kale cudurka viral. Waxaa macquul ah in cudurku uu ka billaabayo si ay u horumariyaan ka dib markii caabuqyada ba'an ee neef-mareenka iyo caloosha ama in bukaanlayda qaadato antibiotics. Iyadoo la tixgelinayo pathogenesis ee HUS, saaraysa, muhiimada ugu weyn ee ku lifaaqan joogitaanka reactions, shalalka. Xaaladaha qaarkood, waxay xitaa ku siin karaan kor u microangiopathy systemic.

symptomatology

Waa maxay calaamadaha waxaa inta badan sababa hemolytic uremiskt syndrom? Waa in la ogaadaa in koorsada cudurka by dhakhaatiirta conventionally kala qaybiyey saddex caadada. First, prodromal, socon karaa hal maalin ilaa laba toddobaad. Second, ee loo yaqaan "muddada dhibaatada" - oo ka mid ah saddex todobaad. Markaas yimaado muddo ka soo kabashada (ama dhimasho) ee bukaanka.

Qaybta koowaad ee cudurka oo dhan ekaan sumowga iyo waxaa la socda calaamado sida matag, calool xanuun aad u daran, shuban la raad dhiig. Bukaanjiifka qaar marxaladan calaamadeeyay gariir, lulmo iyo xataa miyirka oo luma. Ka dib markii a muddo prodromal in bukaan badan yimaaddo kabashada a arki karo. Iyadoo syndrome takhasusay haemolytic hemolytiskt la xidhiidha sida dhiig haemolytic, Torombositobiiniya, iyo lesions kelyaha. Dhakhaatiirta ayaa sheegay in in sawirka caafimaad, sida caadiga ah, kala duwanaayeen polymorphism ah. In bukaanka qaar ka mid ah, astaamaha xukumaan laga yaabaa in dhibaatooyinka hemolytic, dadka kale - calaamado ba'an kelyaha. Caadi ah in dhammaan kiisaska loo arkaa calaamad u ah dhiig hemolytic - waxa ay u muuqataa in dhex HUS ah.

Hemolytic-uremiskt syndrom carruurta ee marxaladda labaad waxaa lagu gartaa doorsoonka ah dødsregalierne maqaarka. In joogitaanka joonis lagu ogaan karaa hyperbilirubinemia. imtixaanka Direct Coombs 'caadiga ah waa negative, hemoglobin hoos u, tirada erythrocytes dhimay. Sidoo kale, bukaanka inta badan sanka dhiig.

Baadhista xanuunada

Dhakhaatiirta badanaa ogaado HUS, ku salaysan saddex qodob oo waaweyn: joogitaanka dhiig hemolytic, purpura Torombositobiiniya iyo uremia. Guud ahaan, sawir caafimaad waa garabaka Moshkovitsa syndrome (cudur kalyaha ah, dhiig xinjiro weelasha, iyo D. sidaas on.), Iyadoo farqiga kaliya in ay in dambaysta ah waxaa inta badan lagu arkaa carruurta waaweyn, iyo mikrotrombozov badanaa ku dhacda wadnaha iyo beerka.

Hemolytic uremiskt syndrom, daaweynta

autoaggression Xakamaynta - in goolkii ugu weyn ee daaweynta. Sida caadiga ah, dhakhaatiirta dibadda u diray ciidamada oo dhan si looga hortago xinjirowga intravascular. Well caawin heparin iyo prednisolone. Haddii aanu dawada caawin, waxa ay muujineysaa kelyaha.